Click here to close
Hello! We notice that you are using Internet Explorer, which is not supported by Xenbase and may cause the site to display incorrectly.
We suggest using a current version of Chrome,
FireFox, or Safari.
Mol Cell
2011 May 20;424:500-10. doi: 10.1016/j.molcel.2011.04.018.
Show Gene links
Show Anatomy links
Identification of a microRNA that activates gene expression by repressing nonsense-mediated RNA decay.
Bruno IG
,
Karam R
,
Huang L
,
Bhardwaj A
,
Lou CH
,
Shum EY
,
Song HW
,
Corbett MA
,
Gifford WD
,
Gecz J
,
Pfaff SL
,
Wilkinson MF
.
???displayArticle.abstract???
Nonsense-mediated decay (NMD) degrades both normal and aberrant transcripts harboring stop codons in particular contexts. Mutations that perturb NMD cause neurological disorders in humans, suggesting that NMD has roles in the brain. Here, we identify a brain-specific microRNA-miR-128-that represses NMD and thereby controls batteries of transcripts in neural cells. miR-128 represses NMD by targeting the RNA helicase UPF1 and the exon-junction complex core component MLN51. The ability of miR-128 to regulate NMD is a conserved response occurring in frogs, chickens, and mammals. miR-128 levels are dramatically increased in differentiating neuronal cells and during brain development, leading to repressed NMD and upregulation of mRNAs normally targeted for decay by NMD; overrepresented are those encoding proteins controlling neuron development and function. Together, these results suggest the existence of a conserved RNA circuit linking the microRNA and NMD pathways that induces cell type-specific transcripts during development.
Abu-Elneel,
Heterogeneous dysregulation of microRNAs across the autism spectrum.
2008, Pubmed
Abu-Elneel,
Heterogeneous dysregulation of microRNAs across the autism spectrum.
2008,
Pubmed
Addington,
A novel frameshift mutation in UPF3B identified in brothers affected with childhood onset schizophrenia and autism spectrum disorders.
2011,
Pubmed
Anastasaki,
Dhx34 and Nbas function in the NMD pathway and are required for embryonic development in zebrafish.
2011,
Pubmed
Bak,
MicroRNA expression in the adult mouse central nervous system.
2008,
Pubmed
Bartel,
MicroRNAs: target recognition and regulatory functions.
2009,
Pubmed
Béïque,
Arc-dependent synapse-specific homeostatic plasticity.
2011,
Pubmed
Bhuvanagiri,
NMD: RNA biology meets human genetic medicine.
2010,
Pubmed
Cao,
A functional study of miR-124 in the developing neural tube.
2007,
Pubmed
Chan,
A UPF3-mediated regulatory switch that maintains RNA surveillance.
2009,
Pubmed
Chan,
An alternative branch of the nonsense-mediated decay pathway.
2007,
Pubmed
Chang,
The nonsense-mediated decay RNA surveillance pathway.
2007,
Pubmed
Cheng,
Stage-dependent STAT3 activation is involved in the differentiation of rat hippocampus neural stem cells.
2011,
Pubmed
Giorgi,
The EJC factor eIF4AIII modulates synaptic strength and neuronal protein expression.
2007,
Pubmed
Godlewski,
Targeting of the Bmi-1 oncogene/stem cell renewal factor by microRNA-128 inhibits glioma proliferation and self-renewal.
2008,
Pubmed
Haremaki,
Regulation of vertebrate embryogenesis by the exon junction complex core component Eif4a3.
2010,
Pubmed
,
Xenbase
Hogg,
Upf1 senses 3'UTR length to potentiate mRNA decay.
2010,
Pubmed
Hsu,
miRNAMap: genomic maps of microRNA genes and their target genes in mammalian genomes.
2006,
Pubmed
Humphrey,
Molecular cloning and characterization of the chicken cationic amino acid transporter-2 gene.
2008,
Pubmed
Kapsimali,
MicroRNAs show a wide diversity of expression profiles in the developing and mature central nervous system.
2007,
Pubmed
Kim,
A MicroRNA feedback circuit in midbrain dopamine neurons.
2007,
Pubmed
Kulozik,
Stay tuned: miRNA expression and nonsense-mediated decay in brain development.
2011,
Pubmed
Laumonnier,
Mutations of the UPF3B gene, which encodes a protein widely expressed in neurons, are associated with nonspecific mental retardation with or without autism.
2010,
Pubmed
Lee,
Altered microRNA regulation in Huntington's disease models.
2011,
Pubmed
Le Guiner,
TIA-1 or TIAR is required for DT40 cell viability.
2003,
Pubmed
Long,
The nonsense-mediated decay pathway maintains synapse architecture and synaptic vesicle cycle efficacy.
2010,
Pubmed
Lukiw,
Micro-RNA speciation in fetal, adult and Alzheimer's disease hippocampus.
2007,
Pubmed
McIlwain,
Smg1 is required for embryogenesis and regulates diverse genes via alternative splicing coupled to nonsense-mediated mRNA decay.
2010,
Pubmed
Medghalchi,
Rent1, a trans-effector of nonsense-mediated mRNA decay, is essential for mammalian embryonic viability.
2001,
Pubmed
Mendell,
Nonsense surveillance regulates expression of diverse classes of mammalian transcripts and mutes genomic noise.
2004,
Pubmed
Nakanaga,
Autotaxin--an LPA producing enzyme with diverse functions.
2010,
Pubmed
Pacheco,
Diversity of vertebrate splicing factor U2AF35: identification of alternatively spliced U2AF1 mRNAS.
2004,
Pubmed
Patil,
Novel gene ashwin functions in Xenopus cell survival and anteroposterior patterning.
2006,
Pubmed
,
Xenbase
Ramocki,
Failure of neuronal homeostasis results in common neuropsychiatric phenotypes.
2008,
Pubmed
Rebbapragada,
Execution of nonsense-mediated mRNA decay: what defines a substrate?
2009,
Pubmed
Rehwinkel,
Nonsense-mediated mRNA decay: Target genes and functional diversification of effectors.
2006,
Pubmed
Saba,
A miRNA signature of prion induced neurodegeneration.
2008,
Pubmed
Sempere,
Expression profiling of mammalian microRNAs uncovers a subset of brain-expressed microRNAs with possible roles in murine and human neuronal differentiation.
2004,
Pubmed
Silver,
The exon junction complex component Magoh controls brain size by regulating neural stem cell division.
2010,
Pubmed
Smirnova,
Regulation of miRNA expression during neural cell specification.
2005,
Pubmed
Tarpey,
Mutations in UPF3B, a member of the nonsense-mediated mRNA decay complex, cause syndromic and nonsyndromic mental retardation.
2007,
Pubmed
Weischenfeldt,
NMD is essential for hematopoietic stem and progenitor cells and for eliminating by-products of programmed DNA rearrangements.
2008,
Pubmed
Wittkopp,
Nonsense-mediated mRNA decay effectors are essential for zebrafish embryonic development and survival.
2009,
Pubmed
Zhang,
MicroRNA-128 inhibits glioma cells proliferation by targeting transcription factor E2F3a.
2009,
Pubmed