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Allard,
When muscle Ca2+ channels carry monovalent cations through gating pores: insights into the pathophysiology of type 1 hypokalaemic periodic paralysis.
2018, Pubmed
Allard,
When muscle Ca2+ channels carry monovalent cations through gating pores: insights into the pathophysiology of type 1 hypokalaemic periodic paralysis.
2018,
Pubmed
Campos,
Two atomic constraints unambiguously position the S4 segment relative to S1 and S2 segments in the closed state of Shaker K channel.
2007,
Pubmed
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Xenbase
Cannon,
Channelopathies of skeletal muscle excitability.
2015,
Pubmed
Cannon,
Voltage-sensor mutations in channelopathies of skeletal muscle.
2010,
Pubmed
Cannon,
An atypical CaV1.1 mutation reveals a common mechanism for hypokalemic periodic paralysis.
2017,
Pubmed
Chahine,
Improving the characterization of calcium channel gating pore currents with Stac3.
2018,
Pubmed
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Xenbase
Collet,
Intramembrane charge movement and L-type calcium current in skeletal muscle fibers isolated from control and mdx mice.
2003,
Pubmed
Fuster,
Elevated resting H+ current in the R1239H type 1 hypokalaemic periodic paralysis mutated Ca2+ channel.
2017,
Pubmed
Fuster,
Na leak with gating pore properties in hypokalemic periodic paralysis V876E mutant muscle Ca channel.
2017,
Pubmed
Jurkat-Rott,
Pathophysiological role of omega pore current in channelopathies.
2012,
Pubmed
Jurkat-Rott,
K+-dependent paradoxical membrane depolarization and Na+ overload, major and reversible contributors to weakness by ion channel leaks.
2009,
Pubmed
Jurkat-Rott,
A calcium channel mutation causing hypokalemic periodic paralysis.
1994,
Pubmed
Lefebvre,
Whole-cell voltage clamp on skeletal muscle fibers with the silicone-clamp technique.
2014,
Pubmed
Matthews,
Muscle channelopathies: does the predicted channel gating pore offer new treatment insights for hypokalaemic periodic paralysis?
2010,
Pubmed
Moreau,
Biophysics, pathophysiology, and pharmacology of ion channel gating pores.
2014,
Pubmed
Polster,
Stac adaptor proteins regulate trafficking and function of muscle and neuronal L-type Ca2+ channels.
2015,
Pubmed
Polster,
Stac3 has a direct role in skeletal muscle-type excitation-contraction coupling that is disrupted by a myopathy-causing mutation.
2016,
Pubmed
Ptácek,
Dihydropyridine receptor mutations cause hypokalemic periodic paralysis.
1994,
Pubmed
Rüdel,
Hypokalemic periodic paralysis: in vitro investigation of muscle fiber membrane parameters.
1984,
Pubmed
Ruff,
Insulin acts in hypokalemic periodic paralysis by reducing inward rectifier K+ current.
1999,
Pubmed
Sokolov,
Ion permeation through a voltage- sensitive gating pore in brain sodium channels having voltage sensor mutations.
2005,
Pubmed
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Xenbase
Starace,
A proton pore in a potassium channel voltage sensor reveals a focused electric field.
2004,
Pubmed
Struyk,
A Na+ channel mutation linked to hypokalemic periodic paralysis exposes a proton-selective gating pore.
2007,
Pubmed
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Xenbase
Tombola,
Voltage-sensing arginines in a potassium channel permeate and occlude cation-selective pores.
2005,
Pubmed
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Xenbase
Ursu,
Altered inactivation of Ca2+ current and Ca2+ release in mouse muscle fibers deficient in the DHP receptor gamma1 subunit.
2004,
Pubmed
Wu,
A calcium channel mutant mouse model of hypokalemic periodic paralysis.
2012,
Pubmed
Wu,
Stac3 enhances expression of human CaV1.1 in Xenopus oocytes and reveals gating pore currents in HypoPP mutant channels.
2018,
Pubmed
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Xenbase
